Аннотация:Vein of Galen aneurysmal malformations are special kind of AVMs, which occur mainly in the pediatric group of patients. VGAMs account for about 30% of vascular malformations in the childhood. This pathology has congenital nature and is characterized by the formation of arteriovenous shunt in the area of one of the main venous collector – a vein of Galen. The main clinical manifestations are hypertension-hydrocephalic syndrome, delayed psychomotor development, and focal neurological symptoms. VGAMs often combine with malformations of the heart and vascular system. Currently, the standard diagnostics of VGAMs should include ultrasound, which allows to make accurate diagnosis already in the third trimester of pregnancy. More detailed information can be obtained by transcranial Doppler ultrasonography, computed tomography, magnetic resonance imaging, magnetic resonance angiography, and cerebral angiography. At the present stage of development of vascular neurosurgery, the treatment of choice of VGAMs is endovascular surgery. The indications for endovascular treatment are the presence of available afferents of VGAM for the occlusion. The method of the occlusion must be selected individually for each patient after a thorough analysis of the angioarchitectonics of VGAM. For the best results of treatment, patients should undergo surgery within the first months of life. Microsurgical resection of VGAMs is associated with a high risk of intraoperative complications. Radiosurgical treatment in the presence of dilatation of the vein of Galen and large afferents is ineffective. Shunting procedures can be performed in patients with VGAMs in some cases.